Final Diagnosis -- Polycystic disease (Hematuria and Azotemia)
- PART 1: NATIVE LIVER FROM ORTHOTOPIC TRANSPLANT PROCEDURE-
- A. POLYCYSTIC LIVER DISEASE (33.6 POUNDS) WITH
MULTIPLE VON MEYENBERG COMPLEXES.
- B. ATHEROSCLEROTIC CHANGES INVOLVING THE HEPATIC
ARTERY.
- C. INTIMAL THICKENING AND MYXOID CHANGE IN THE PORTAL
VEINS.
- D. GALLBLADDER WITH AUTOLYTIC CHANGE, MINIMAL CHRONIC
INFLAMMATION AND FIBROSIS.
- PART 2: LEFT KIDNEY, NEPHRECTOMY-
- A. POLYCYSTIC KIDNEY DISEASE (1430 GM).
- B. ATHEROSCLEROSIS OF RENAL ARTERY AND ITS
INTRA-RENAL BRANCHES.
- PART 3: SPLEEN, SPLENECTOMY-
CONGESTED SPLEEN (130 GM) WITH CYSTIC CHANGE.
ADDENDUM #1
Immunohistochemical markers showed the splenic cysts to be lined
by mostly Factor-VIII positive cells. Focal staining for AE1/AE3
was also occasionally demonstrable, but, is of questionable
significance. These findings suggest that the cysts observed in
the spleen may represent hemangiomas.